CRANIOSYNOSTOSIS: EARLY RECOGNITION PREVENTS FATAL COMPLICATIONS
Abstract
Background: Craniosynostosis is the premature fusion of cranial vault sutures. The overallincidence is 3-5/10,000 live births. With multiple craniosynostoses, brain growth may be impeded
by the unyielding skull. Most cases of single suture involvement can be treated with linear
excision of suture. Involvement of multiple sutures or skull has usually required combined efforts
of neurosurgeons and craniofacial surgeons. Methods: On the basis of visible skull deformity all
patients were admitted in the Department of Neurosurgery, Liaquat University Hospital,
Jamshoro, Pakistan. Patients were examined for signs of raised ICP and other congenital
deformities. The records of patients were maintained till follow up. Results: Twenty-seven
children were included in this study from 2002 to 2009. Age range was 1-6 years, boys were 18
(66.6%), and girls were 9 (33.3%). The common suture affected was coronal 12 (44.4%). Two
children with craniostenosis belonged to same family, and all presented with suture involvement.
Three (11.1%) deaths occurred due to hypothermia (1), and blood loss (2). Conclusion: Early
diagnosis, expert surgical techniques and per- and postoperative care for bleeding and temperature
regulation prevent mortality and morbidity.
Keywords: Craniosynostosis, children, skull defects, suture
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